Primary cutaneous blastic natural killer cell lymphoma.

نویسندگان

  • Eric C Parlette
  • J Zachary Elliott
  • Frank W Hall
  • Bradley S Graham
چکیده

Sir, Blastic natural killer-cell lymphoma, also called “agranular CD4+ CD56+ haematodermic neoplasm” is an uncommon type of tumour, which is included in the new World Health Organization (WHO) classification as a malignancy derived from natural killer (NK) cells. It is very aggressive, affecting many organs, and skin involvement is highly characteristic. Several origins have been proposed, but recent studies have shown a relationship with plasmocytoid monocytes. We report here a new case of this rare lymphoma, with skin infiltration as the first manifestation, and with early dissemination to bone marrow and central nervous system (CNS).

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عنوان ژورنال:
  • Journal of the American Academy of Dermatology

دوره 53 4  شماره 

صفحات  -

تاریخ انتشار 2005